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Types of soft tissue sarcoma

Angiosarcoma of the heart

Angiosarcoma is a rare type of soft tissue sarcoma. It is a type of vascular tumour. Vascular tumours develop from endothelial cells. These cells make up the walls of blood or .

Most tumours that start in the heart are  . About 10 out of 100 (10%) are . Most commonly these are soft tissue sarcomas.

Read more about soft tissue sarcoma

Causes

We don’t know what causes angiosarcoma of the heart. Some of these cancers have been linked to past radiotherapy treatment. But as it is such a rare cancer, it is difficult to find a common cause.

Read more about risks and causes

Symptoms

Symptoms can vary depending on where in the heart the cancer is. Many people don’t have any symptoms until the cancer has spread to other parts of the body (advanced disease).

Symptoms can include:

  • chest pain

  • feeling like you want to faint or fainting

  • tiredness

When symptoms do happen, they can be similar to those caused by heart failure. They may include breathlessness, chest pain, or fluid on the lung ( ).

Sometimes a small piece of the tumour can break off and form a small clump or clot that blocks a . This is called an embolism. If an embolism travels through the bloodstream, it can block a blood vessel near the heart, causing pain.

Embolisms can also travel to other parts of the body, such as the brain, causing a .

Tests

Your doctor will examine you. You might have one or more of these tests: 

  • an

  • an ultrasound to look at the valves and structure of the heart (an )

  • an ECG ( )

Find out more about these tests

Treatment

The main treatment for angiosarcoma of the heart is surgery. Your surgeon aims to remove as much of the cancer as possible, with a border of healthy tissue (margin) around it. Having a border of healthy tissue without any cancer cells is important. It aims to lower the risk of angiosarcoma coming back in the same place. 

Unfortunately, it is not always possible to completely remove the cancer. It depends on the size of the sarcoma, and where it is in your heart. 

You might also have radiotherapy or chemotherapy as part of your treatment. 

If your sarcoma has spread 

Sadly, angiosarcoma of the heart often grows quickly. In most people diagnosed, the sarcoma has already spread to other parts of the body. The most common place for it to spread is the lungs. In this situation, surgery will not cure it.

The doctor may offer other treatment to try and control the disease and relieve any symptoms for a time.

Read more about the different treatment types

Coping

Coping with a diagnosis of a rare cancer can be especially difficult. Knowing more about your sarcoma and its treatment can make it easier. It can help you to make decisions and cope with what happens.

Sarcoma UK has support and information for people affected by soft tissue and bone sarcoma.

Visit the Sarcoma UK website

The Rare Cancer Alliance offer support and information to people with rare cancers.

Visit the Rare Cancer Alliance website

Talking to other people who have the same thing can also help.

Our discussion forum Cancer Chat is a place for anyone affected by cancer. You can share experiences, stories and information with other people who know what you are going through.

Visit Cancer Chat

Last reviewed: 15 Aug 2024

Next review due: 15 Aug 2027

Getting diagnosed with soft tissue sarcoma

You usually start by seeing your GP. They will examine you and might refer you for tests or to a specialist.

Treatment for soft tissue sarcoma

The main treatment for soft tissue sarcoma is surgery. You may also have radiotherapy treatment to reduce the symptoms and help you feel better. A team of doctors and other professionals discuss the best treatment and care for you.

Living with soft tissue sarcoma

Lots of advice and support are available to help you cope with soft tissue sarcoma and its treatment.

Soft tissue sarcoma main page

Soft tissue sarcoma cancers develop in the supporting tissues of the body. Find out about symptoms, causes, types, treatment, and more.

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